Number of the records: 1
dysplázia ektodermálna
Record number d004476 Date 06.06.2025 Type M - MESH Topical term dysplázia ektodermálna Other term English (Pseudonym) Anhidrotic Ectodermal Dysplasia
English (Pseudonym) Aplasia Cutis Congenita
English (Pseudonym) Clouston's Syndrome
English (Pseudonym) Ectodermal Defect, Congenital
English (Pseudonym) Hidrotic Ectodermal Dysplasia
Slovak (Pseudonym) dysplázia ektodermová
Slovak (Pseudonym) dysplázia ektodermová anhidrotická
Slovak (Pseudonym) dysplázia ektodermálna anhidrotická
Slovak (Pseudonym) aplasia cutis congenita
Slovak (Pseudonym) Cloustonov syndróm
Slovak (Pseudonym) defekt ektodermový kongenitálny
Slovak (Pseudonym) dysplázia ektodermová hidrotická
UDC C16.131.077.350C16.131.831.350C16.320.850.250C17.800.804.350C17.800.827.250 Note A group of hereditary disorders involving tissues and structures derived from the embryonic ectoderm. They are characterized by the presence of abnormalities at birth and involvement of both the epidermis and skin appendages. They are generally nonprogressive and diffuse. Various forms exist, including anhidrotic and hidrotic dysplasias, FOCAL DERMAL HYPOPLASIA, and aplasia cutis congenita. subject heading
Number of the records: 1