Number of the records: 1  

hemoglobinúria paroxyzmálna

  1. Record numberd006457
    Date06.06.2025
    TypeM
    Topical termhemoglobinúria paroxyzmálna
    Other termEnglish (Pseudonym) Paroxysmal Cold Hemoglobinuria
    English (Pseudonym) Paroxysmal Nocturnal Hemoglobinuria
    Slovak (Pseudonym) hemoglobinúria paroxyzmálna chladová
    Slovak (Pseudonym) hemoglobinúria paroxyzmálna nočná
    UDCC15.378.050.141.560C15.378.190.625.460
    NoteA condition characterized by the recurrence of HEMOGLOBINURIA caused by intravascular HEMOLYSIS. In cases occurring upon cold exposure (paroxysmal cold hemoglobinuria), usually after infections, there is a circulating antibody which is also a cold hemolysin. In cases occurring during or after sleep (paroxysmal nocturnal hemoglobinuria), the clonal hematopoietic stem cells exhibit a global deficiency of cell membrane proteins.
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Number of the records: 1  

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