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hemoglobinúria paroxyzmálna
Record number d006457 Date 06.06.2025 Type M Topical term hemoglobinúria paroxyzmálna Other term English (Pseudonym) Paroxysmal Cold Hemoglobinuria
English (Pseudonym) Paroxysmal Nocturnal Hemoglobinuria
Slovak (Pseudonym) hemoglobinúria paroxyzmálna chladová
Slovak (Pseudonym) hemoglobinúria paroxyzmálna nočná
UDC C15.378.050.141.560C15.378.190.625.460 Note A condition characterized by the recurrence of HEMOGLOBINURIA caused by intravascular HEMOLYSIS. In cases occurring upon cold exposure (paroxysmal cold hemoglobinuria), usually after infections, there is a circulating antibody which is also a cold hemolysin. In cases occurring during or after sleep (paroxysmal nocturnal hemoglobinuria), the clonal hematopoietic stem cells exhibit a global deficiency of cell membrane proteins. subject heading
Number of the records: 1