Number of the records: 1
polyendokrinopatie autoimunitné
Record number d016884 Date 06.06.2025 Type M Topical term polyendokrinopatie autoimunitné Other term English (Pseudonym) Autoimmune Polyendocrinopathy-Candidiasis-Ectodermal-Dystrophy
English (Pseudonym) Autoimmune Syndrome Type II, Polyglandular
English (Pseudonym) Autoimmune Syndrome Type I, Polyglandular
English (Pseudonym) Polyglandular Type I Autoimmune Syndrome
English (Pseudonym) Polyglandular Type II Autoimmune Syndrome
English (Pseudonym) Schmidt's Syndrome
Slovak (Pseudonym) polyendokrinopatia-kandidiáza-ektodermálna dystrofia, autoimunitná
Slovak (Pseudonym) polyendokrinopatia-kandidóza-ektodermová dystrofia, autoimunitná
Slovak (Pseudonym) syndróm autoimunitný polyendokrinný, typ 2
Slovak (Pseudonym) syndróm autoimunitnej polyendokrinopatie, typ 1
Slovak (Pseudonym) syndróm polyglandulárny autoimunitný, typ I
Slovak (Pseudonym) syndróm polyglandulárny autoimunitný typu I
Slovak (Pseudonym) syndróm polyglandulárny autoimunitný, typ II
Slovak (Pseudonym) syndróm polyglandulárny autoimunitný typu II
Slovak (Pseudonym) diabetes mellitus, Addisonova choroba, myxedém
Slovak (Pseudonym) syndróm viacpočetnej endokrinnej deficiencie, typ 2
Slovak (Pseudonym) syndróm polyglandulárnej deficiencie, typ 2
Slovak (Pseudonym) Schmidtov syndróm
UDC C19.787C20.111.750 Note Autoimmune diseases affecting multiple endocrine organs. Type I is characterized by childhood onset and chronic mucocutaneous candidiasis (CANDIDIASIS, CHRONIC MUCOCUTANEOUS), while type II exhibits any combination of adrenal insufficiency (ADDISON'S DISEASE), lymphocytic thyroiditis (THYROIDITIS, AUTOIMMUNE;), HYPOPARATHYROIDISM; and gonadal failure. In both types organ-specific ANTIBODIES against a variety of ENDOCRINE GLANDS have been detected. The type II syndrome differs from type I in that it is associated with HLA-A1 and B8 haplotypes, onset is usually in adulthood, and candidiasis is not present. subject heading
Number of the records: 1