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polyendokrinopatie autoimunitné

  1. Record numberd016884
    Date06.06.2025
    TypeM
    Topical termpolyendokrinopatie autoimunitné
    Other termEnglish (Pseudonym) Autoimmune Polyendocrinopathy-Candidiasis-Ectodermal-Dystrophy
    English (Pseudonym) Autoimmune Syndrome Type II, Polyglandular
    English (Pseudonym) Autoimmune Syndrome Type I, Polyglandular
    English (Pseudonym) Polyglandular Type I Autoimmune Syndrome
    English (Pseudonym) Polyglandular Type II Autoimmune Syndrome
    English (Pseudonym) Schmidt's Syndrome
    Slovak (Pseudonym) polyendokrinopatia-kandidiáza-ektodermálna dystrofia, autoimunitná
    Slovak (Pseudonym) polyendokrinopatia-kandidóza-ektodermová dystrofia, autoimunitná
    Slovak (Pseudonym) syndróm autoimunitný polyendokrinný, typ 2
    Slovak (Pseudonym) syndróm autoimunitnej polyendokrinopatie, typ 1
    Slovak (Pseudonym) syndróm polyglandulárny autoimunitný, typ I
    Slovak (Pseudonym) syndróm polyglandulárny autoimunitný typu I
    Slovak (Pseudonym) syndróm polyglandulárny autoimunitný, typ II
    Slovak (Pseudonym) syndróm polyglandulárny autoimunitný typu II
    Slovak (Pseudonym) diabetes mellitus, Addisonova choroba, myxedém
    Slovak (Pseudonym) syndróm viacpočetnej endokrinnej deficiencie, typ 2
    Slovak (Pseudonym) syndróm polyglandulárnej deficiencie, typ 2
    Slovak (Pseudonym) Schmidtov syndróm
    UDCC19.787C20.111.750
    NoteAutoimmune diseases affecting multiple endocrine organs. Type I is characterized by childhood onset and chronic mucocutaneous candidiasis (CANDIDIASIS, CHRONIC MUCOCUTANEOUS), while type II exhibits any combination of adrenal insufficiency (ADDISON'S DISEASE), lymphocytic thyroiditis (THYROIDITIS, AUTOIMMUNE;), HYPOPARATHYROIDISM; and gonadal failure. In both types organ-specific ANTIBODIES against a variety of ENDOCRINE GLANDS have been detected. The type II syndrome differs from type I in that it is associated with HLA-A1 and B8 haplotypes, onset is usually in adulthood, and candidiasis is not present.
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Number of the records: 1  

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