Number of the records: 1  

ichtyóza lamelárna

  1. Record numberd017490
    Date09.07.2025
    TypeM - MESH
    Topical termichtyóza lamelárna
    Other termEnglish (Pseudonym) Erythroderma Ichthyosiforme, Nonbullous
    English (Pseudonym) Harlequin Fetus
    English (Pseudonym) Ichthyosiform Erythroderma, Nonbullous Congenital
    Slovak (Pseudonym) erythrodermia ichthyosiformis nonbullosa
    Slovak (Pseudonym) Harlequin fetus
    Slovak (Pseudonym) ichthyosis congenita gravis
    Slovak (Pseudonym) collodion fetus
    Slovak (Pseudonym) ichtyóza kongenitálna
    Slovak (Pseudonym) deskvamácia novorodenecká
    Slovak (Pseudonym) erytrodermia ichtyoziformná nebulózna vrodená
    Slovak (Pseudonym) erytrodermia ichtyoziformná nebulózna kongenitálna
    Slovak (Pseudonym) erytrodermia ichtyoziformná nebulózna
    Slovak (Pseudonym) erytrodermia ichtyoziformná nonbulózna kongenitálna
    Slovak (Pseudonym) plod Harlekýn
    Slovak (Pseudonym) plod harlekýn
    Slovak (Pseudonym) ichtyóza Harlekýn
    Slovak (Pseudonym) ichtyóza harlekýn
    Slovak (Pseudonym) ichtyóza kongenitálna I
    Slovak (Pseudonym) ichtyóza kongenitálna II
    Slovak (Pseudonym) ichtyóza vrodená
    Slovak (Pseudonym) ichtyóza lamelárna, typ 1
    Slovak (Pseudonym) ichtyóza lamelárna 1
    Slovak (Pseudonym) ichtyóza lamelárna nebulózna kongenitálna
    Slovak (Pseudonym) ichtyózy lamelárne
    Slovak (Pseudonym) deskvamácia neonatálna
    Slovak (Pseudonym) exfoliácia lamelárna novorodenecká
    Slovak (Pseudonym) Harlekýn syndróm
    Slovak (Pseudonym) syndróm bábätka harlekýn
    Slovak (Pseudonym) ichtyóza typu collodion-baby
    UDCC16.131.831.512.400.410C16.320.850.400.410C16.614.492.400.410C17.800.428.333.250.410C17.800.804.512.400.410C17.800.827.400.410
    NoteA chronic, congenital ichthyosis inherited as an autosomal recessive trait. Infants are usually born encased in a collodion membrane which sheds within a few weeks. Scaling is generalized and marked with grayish-brown quadrilateral scales, adherent at their centers and free at the edges. In some cases, scales are so thick that they resemble armored plate.
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Number of the records: 1  

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