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neoplázia endokrinná mnohopočetná, typ 2b
Record number d018814 Date 06.06.2025 Type M Topical term neoplázia endokrinná mnohopočetná, typ 2b Other term English (Pseudonym) MEN 2b
English (Pseudonym) MEN 3
English (Pseudonym) Neoplasia, Multiple Endocrine Type 2b
English (Pseudonym) Neoplasms, Multiple Endocrine Type 2b
Slovak (Pseudonym) nádory endokrinné mnohopočetné, typ 2b
Slovak (Pseudonym) MEN2b
Slovak (Pseudonym) MEN 2b
Slovak (Pseudonym) MEN 3
See also (Later heading) feochromocytóm
(Later heading) karcinóm medulárny
UDC C04.588.322.400.510C04.651.600.510C04.700.630.510C16.320.700.630.510C19.344.400.510 Note Similar to MEN2A, it is also caused by mutations of the MEN2 gene, also known as the RET proto-oncogene. Its clinical symptoms include medullary carcinoma (CARCINOMA, MEDULLARY) of THYROID GLAND and PHEOCHROMOCYTOMA of ADRENAL MEDULLA (50%). Unlike MEN2a, MEN2b does not involve PARATHYROID NEOPLASMS. It can be distinguished from MEN2A by its neural abnormalities such as mucosal NEUROMAS on EYELIDS; LIP; and TONGUE, and ganglioneuromatosis of GASTROINTESTINAL TRACT leading to MEGACOLON. It is an autosomal dominant inherited disease. subject heading
Number of the records: 1