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komora ľavá nekompaktná izolovaná

  1. Record numberd056830
    Date06.06.2025
    TypeM
    Topical termkomora ľavá nekompaktná izolovaná
    Other termEnglish (Pseudonym) Isolated Noncompaction of the Left Ventricular Myocardium, X-Linked
    English (Pseudonym) Isolated Non-compaction of the Ventricular Myocardium
    English (Pseudonym) Noncompaction of the Left Ventricular Myocardium, Autosomal Dominant
    Slovak (Pseudonym) nonkompakcia srdcovej komory, izolovaná
    Slovak (Pseudonym) non-kompakcia srdcovej komory, izolovaná
    Slovak (Pseudonym) nekompakcia myokardu ľavej komory, izolovaná
    Slovak (Pseudonym) nonkompakcia myokardu ľavej komory, izolovaná, viazaná na X-chromozóm
    Slovak (Pseudonym) nonkompakcia myokardu ľavej komory, izolovaná, autozomálne dominantná
    Slovak (Pseudonym) nonkompakcia myokardu ľavej komory, izolovaná, autozómovo dominantná
    See also(Later heading) Barthov syndróm
    UDCC14.240.400.660C14.280.238.281.500C14.280.400.660C16.131.077.477C16.131.240.400.655C16.320.322.370
    NoteRare congenital cardiomyopathies characterized by the lack of left ventricular myocardium compaction. The noncompaction results in numerous prominent trabeculations and a loose myocardial meshwork (spongy myocardium) in the LEFT VENTRICLE. Heterogeneous clinical features include diminished systolic function sometimes associated with left ventricular dilation, that presents either neonatally or progressively. Often, the RIGHT VENTRICLE is also affected. CONGESTIVE HEART FAILURE; PULMONARY EMBOLISM; and ventricular ARRHYTHMIA are commonly seen.
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Number of the records: 1  

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