Number of the records: 1
komora ľavá nekompaktná izolovaná
Record number d056830 Date 06.06.2025 Type M Topical term komora ľavá nekompaktná izolovaná Other term English (Pseudonym) Isolated Noncompaction of the Left Ventricular Myocardium, X-Linked
English (Pseudonym) Isolated Non-compaction of the Ventricular Myocardium
English (Pseudonym) Noncompaction of the Left Ventricular Myocardium, Autosomal Dominant
Slovak (Pseudonym) nonkompakcia srdcovej komory, izolovaná
Slovak (Pseudonym) non-kompakcia srdcovej komory, izolovaná
Slovak (Pseudonym) nekompakcia myokardu ľavej komory, izolovaná
Slovak (Pseudonym) nonkompakcia myokardu ľavej komory, izolovaná, viazaná na X-chromozóm
Slovak (Pseudonym) nonkompakcia myokardu ľavej komory, izolovaná, autozomálne dominantná
Slovak (Pseudonym) nonkompakcia myokardu ľavej komory, izolovaná, autozómovo dominantná
See also (Later heading) Barthov syndróm
UDC C14.240.400.660C14.280.238.281.500C14.280.400.660C16.131.077.477C16.131.240.400.655C16.320.322.370 Note Rare congenital cardiomyopathies characterized by the lack of left ventricular myocardium compaction. The noncompaction results in numerous prominent trabeculations and a loose myocardial meshwork (spongy myocardium) in the LEFT VENTRICLE. Heterogeneous clinical features include diminished systolic function sometimes associated with left ventricular dilation, that presents either neonatally or progressively. Often, the RIGHT VENTRICLE is also affected. CONGESTIVE HEART FAILURE; PULMONARY EMBOLISM; and ventricular ARRHYTHMIA are commonly seen. subject heading
Number of the records: 1