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syndróm stiff-person

  1. Record numberd016750
    Date06.06.2025
    TypeM - MESH
    Topical termsyndróm stiff-person
    Other termEnglish (Pseudonym) Moersch-Woltmann Syndrome
    English (Pseudonym) Stiff-Man Syndrome
    Slovak (Pseudonym) syndróm stiff-man
    Slovak (Pseudonym) Moerschov-Woltmanov syndróm
    Slovak (Pseudonym) syndróm svalovej stuhnutosti
    Slovak (Pseudonym) syndróm svalovej tuhosti
    Slovak (Pseudonym) syndróm stuhnutej osoby
    Slovak (Pseudonym) hyperekplexia familiárna
    Slovak (Pseudonym) syndróm stuhnutého dieťaťa
    UDCC10.114.812C10.228.854.790C10.668.900C20.111.258.850
    NoteA condition characterized by persistent spasms (SPASM) involving multiple muscles, primarily in the lower limbs and trunk. The illness tends to occur in the fourth to sixth decade of life, presenting with intermittent spasms that become continuous. Minor sensory stimuli, such as noise and light touch, precipitate severe spasms. Spasms do not occur during sleep and only rarely involve cranial muscles. Respiration may become impaired in advanced cases. (Adams et al., Principles of Neurology, 6th ed, p1492; Neurology 1998 Jul;51(1):85-93)
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Number of the records: 1  

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