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ADAMTS13 proteín
Č. záznamu d000071120 Dátum 06.06.2025 Typ M Tematický termín ADAMTS13 proteín Iný termín Slovenčina (Pseudonym) disintegrín a metaloproteináza s proteínom s trombospondínovými motívmi 13
Slovenčina (Pseudonym) ADAMTS-13 proteín
Slovenčina (Pseudonym) ADAMTS13 proteáza
Slovenčina (Pseudonym) proteáza štiepiaca vWF
Slovenčina (Pseudonym) proteináza štiepiaca von Willebrandov faktor
MDT D08.811.277.656.675.374.102.500.813D09.400.430.500.500.813D12.776.395.033.500.813D12.776.860.300.085.813 Poznámka An ADAMTS protease that contains eight thrombospondin (TS) motifs. It cleaves VON WILLEBRAND FACTOR to control vWF-mediated THROMBOSIS. Mutations in the ADAMTS13 gene have been identified in familial cases of PURPURA, THROMBOTIC THROMBOCYTOPENIC and defects in ADAMTS13 activity are associated with MYOCARDIAL INFARCTION; BRAIN ISCHEMIA; PRE-ECLAMPSIA; and MALARIA. predmetové heslo
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