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dermatomyozitída
Č. záznamu d003882 Dátum 06.06.2025 Typ M Tematický termín dermatomyozitída Iný termín Angličtina (Pseudonym) Polymyositis-Dermatomyositis
Slovenčina (Pseudonym) dermatomyositis
Slovenčina (Pseudonym) polymyositis-dermatomyositis
Slovenčina (Pseudonym) polymyozitída-dermatomyozitída
Slovenčina (Pseudonym) dermatopolymyozitída
Pozri tiež (Novšie záhlavie) Malassezia
MDT C05.651.594.819.500C10.668.491.562.575.500C17.300.250C17.800.185 Poznámka A subacute or chronic inflammatory disease of muscle and skin, marked by proximal muscle weakness and a characteristic skin rash. The illness occurs with approximately equal frequency in children and adults. The skin lesions usually take the form of a purplish rash (or less often an exfoliative dermatitis) involving the nose, cheeks, forehead, upper trunk, and arms. The disease is associated with a complement mediated intramuscular microangiopathy, leading to loss of capillaries, muscle ischemia, muscle-fiber necrosis, and perifascicular atrophy. The childhood form of this disease tends to evolve into a systemic vasculitis. Dermatomyositis may occur in association with malignant neoplasms. (From Adams et al., Principles of Neurology, 6th ed, pp1405-6) predmetové heslo
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