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panencefalitída subakútna sklerotizujúca
Č. záznamu d013344 Dátum 06.06.2025 Typ M - MESH Tematický termín panencefalitída subakútna sklerotizujúca Iný termín Angličtina (Pseudonym) Encephalitis, Inclusion Body, Measles
Angličtina (Pseudonym) Leukoencephalitis, Subacute Sclerosing
Angličtina (Pseudonym) Measles Inclusion Body Encephalitis
Angličtina (Pseudonym) Panencephalitis, Subacute Sclerosing
Angličtina (Pseudonym) SSPE
Angličtina (Pseudonym) Van Bogaert's Leukoencephalitis
Slovenčina (Pseudonym) encefalitída spôsobená inklúznymi telieskami vírusu osýpok
Slovenčina (Pseudonym) leukoencefalitída sklerotizujúca subakútna
Slovenčina (Pseudonym) SSPE
Slovenčina (Pseudonym) van Bogaertova leukoencefalitída
Slovenčina (Pseudonym) leukoencefalitída subakútna sklerotizujúca
Slovenčina (Pseudonym) encefalitída osýpková s výskytom inkluzívnych teliesok
Slovenčina (Pseudonym) panencefalitída subakútna sklerotizujúca
Slovenčina (Pseudonym) leucoencephalitis sclerotisans subacuta
Pozri tiež (Novšie záhlavie) vírus osýpok
MDT C01.207.245.340.600C01.207.399.750.600C01.925.182.525.600C01.925.782.580.600.500.500.800C01.925.839.862C10.228.140.430.520.750.600C10.228.228.245.340.600C10.228.228.399.750.600C10.586.250.520.750.600 Poznámka A rare, slowly progressive encephalitis caused by chronic infection with the MEASLES VIRUS. The condition occurs primarily in children and young adults, approximately 2-8 years after the initial infection. A gradual decline in intellectual abilities and behavioral alterations are followed by progressive MYOCLONUS; MUSCLE SPASTICITY; SEIZURES; DEMENTIA; autonomic dysfunction; and ATAXIA. DEATH usually occurs 1-3 years after disease onset. Pathologic features include perivascular cuffing, eosinophilic cytoplasmic inclusions, neurophagia, and fibrous gliosis. It is caused by the SSPE virus, which is a defective variant of MEASLES VIRUS. (From Adams et al., Principles of Neurology, 6th ed, pp767-8) predmetové heslo
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