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syndróm stiff-person
Č. záznamu d016750 Dátum 06.06.2025 Typ M Tematický termín syndróm stiff-person Iný termín Angličtina (Pseudonym) Moersch-Woltmann Syndrome
Angličtina (Pseudonym) Stiff-Man Syndrome
Slovenčina (Pseudonym) syndróm stiff-man
Slovenčina (Pseudonym) Moerschov-Woltmanov syndróm
Slovenčina (Pseudonym) syndróm svalovej stuhnutosti
Slovenčina (Pseudonym) syndróm svalovej tuhosti
Slovenčina (Pseudonym) syndróm stuhnutej osoby
Slovenčina (Pseudonym) hyperekplexia familiárna
Slovenčina (Pseudonym) syndróm stuhnutého dieťaťa
MDT C10.114.812C10.228.854.790C10.668.900C20.111.258.850 Poznámka A condition characterized by persistent spasms (SPASM) involving multiple muscles, primarily in the lower limbs and trunk. The illness tends to occur in the fourth to sixth decade of life, presenting with intermittent spasms that become continuous. Minor sensory stimuli, such as noise and light touch, precipitate severe spasms. Spasms do not occur during sleep and only rarely involve cranial muscles. Respiration may become impaired in advanced cases. (Adams et al., Principles of Neurology, 6th ed, p1492; Neurology 1998 Jul;51(1):85-93) predmetové heslo
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