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prionózy
Č. záznamu d017096 Dátum 06.06.2025 Typ M Tematický termín prionózy Iný termín Angličtina (Pseudonym) Dementias, Transmissible
Angličtina (Pseudonym) Spongiform Encephalopathies, Transmissible
Angličtina (Pseudonym) Transmissible Dementias
Slovenčina (Pseudonym) choroby priónové
Slovenčina (Pseudonym) encefalopatie spongiformné prenosné
Slovenčina (Pseudonym) encefalopatie spongioformné prenosné
Slovenčina (Pseudonym) encefalopatie špongioformné prenosné
Slovenčina (Pseudonym) demencie prenosné
Pozri tiež (Novšie záhlavie) scrapie
(Novšie záhlavie) infekcie pomalé vírusové
MDT C01.207.800C10.228.228.800C10.574.843 Poznámka A group of genetic, infectious, or sporadic degenerative human and animal nervous system disorders associated with abnormal PRIONS. These diseases are characterized by conversion of the normal prion protein to an abnormal configuration via a post-translational process. In humans, these conditions generally feature DEMENTIA; ATAXIA; and a fatal outcome. Pathologic features include a spongiform encephalopathy without evidence of inflammation. The older literature occasionally refers to these as unconventional SLOW VIRUS DISEASES. (From Proc Natl Acad Sci USA 1998 Nov 10;95(23):13363-83) predmetové heslo
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