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glutaryl-CoA-dehydrogenáza
Č. záznamu d050770 Dátum 06.06.2025 Typ M Tematický termín glutaryl-CoA-dehydrogenáza MDT D08.811.682.660.425 Poznámka A flavoprotein enzyme that is responsible for the catabolism of LYSINE; HYDROXYLYSINE; and TRYPTOPHAN. It catalyzes the oxidation of GLUTARYL-CoA to crotonoyl-CoA using FAD as a cofactor. Glutaric aciduria type I is an inborn error of metabolism due to the deficiency of glutaryl-CoA dehydrogenase. predmetové heslo
Počet záznamov: 1