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Schilderova difúzna cerebrálna skleróza

  1. Subject h.Schilderova difúzna cerebrálna skleróza
    Subject h.Diffuse Cerebral Sclerosis of Schilder
    Entry termsAlpersova difúzna degenerácia šedej mozgovej hmoty s cirhózou pečene
    Alpersov syndróm
    Alpersova choroba
    Alpersova progresívna cerebrálna infantilná poliodystrofia
    Alpersova progresívna cerebrálna poliodystrofia detského veku
    Alpersov-Huttenlocherov syndróm
    Balóova koncentrická skleróza
    skleróza mozgová difúzna
    skleróza cerebrálna difúzna
    encephalitis periaxialis
    encefalitída periaxiálna
    encephalitis periaxialis concentrica
    encefalitída periaxiálna koncentrická
    encephalitis periaxialis diffusa
    encefalitída periaxiálna difúzna
    skleróza myelínoklastická difúzna
    poliodystrophia cerebri
    poliodystrofia cerebrálna
    degenerácia progresívna neuronálna, u detí s ochorením pečene
    poliodystrofia progresívna sklerotizujúca
    Schilderova choroba
    skleróza sudanofilná cerebrálna
    English X referencesAlpers Syndrome
    Balo Concentric Sclerosis
    Cerebral Sclerosis, Diffuse
    Encephalitis Periaxialis
    Myelinoclastic Diffuse Sclerosis
    Poliodystrophia Cerebri
    Schilder Disease
    Scope note in EnglishA rare central nervous system demyelinating condition affecting children and young adults. Pathologic findings include a large, sharply defined, asymmetric focus of myelin destruction that may involve an entire lobe or cerebral hemisphere. The clinical course tends to be progressive and includes dementia, cortical blindness, cortical deafness, spastic hemiplegia, and pseudobulbar palsy. Concentric sclerosis of Balo is differentiated from diffuse cerebral sclerosis of Schilder by the pathologic finding of alternating bands of destruction and preservation of myelin in concentric rings. Alpers' Syndrome refers to a heterogeneous group of diseases that feature progressive cerebral deterioration and liver disease. (From Adams et al., Principles of Neurology, 6th ed, p914; Dev Neurosci 1991;13(4-5):267-73)
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