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amyloidóza ľahkých reťazcov

  1. Record numberd000075363
    Date06.06.2025
    TypeM - MESH
    Topical termamyloidóza ľahkých reťazcov
    Other termEnglish (Pseudonym) Monoclonal Immunoglobulin Deposition Disease
    Slovak (Pseudonym) choroba z depozície monoklonových imunoglobulínov
    Slovak (Pseudonym) choroba z ukladania monoklonálnych imunoglobulínov
    Slovak (Pseudonym) AL amyloidóza
    Slovak (Pseudonym) amyloidóza primárna systémová
    Slovak (Pseudonym) amyloidóza z ľahkých reťazcov imunoglobulínu
    Slovak (Pseudonym) amyloidóza primárna
    Slovak (Pseudonym) amyloidóza primárna systémová
    UDCC04.557.595.250C18.452.845.500.550C20.683.515.507C20.683.780.565
    NoteA nonproliferative disorder of PLASMA CELLS characterized by excessive production and misfolding of IMMUNOGLOBULIN LIGHT CHAINS that form insoluble amyloid fibrils (see AMYLOID DEPOSITS) in various tissues. Clinical features include LIVER FAILURE; MULTIPLE MYELOMA; NEPHROTIC SYNDROME; RESTRICTIVE CARDIOMYOPATHY, and neuropathies.
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Number of the records: 1  

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