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amyloidóza ľahkých reťazcov
Record number d000075363 Date 06.06.2025 Type M - MESH Topical term amyloidóza ľahkých reťazcov Other term English (Pseudonym) Monoclonal Immunoglobulin Deposition Disease
Slovak (Pseudonym) choroba z depozície monoklonových imunoglobulínov
Slovak (Pseudonym) choroba z ukladania monoklonálnych imunoglobulínov
Slovak (Pseudonym) AL amyloidóza
Slovak (Pseudonym) amyloidóza primárna systémová
Slovak (Pseudonym) amyloidóza z ľahkých reťazcov imunoglobulínu
Slovak (Pseudonym) amyloidóza primárna
Slovak (Pseudonym) amyloidóza primárna systémová
UDC C04.557.595.250C18.452.845.500.550C20.683.515.507C20.683.780.565 Note A nonproliferative disorder of PLASMA CELLS characterized by excessive production and misfolding of IMMUNOGLOBULIN LIGHT CHAINS that form insoluble amyloid fibrils (see AMYLOID DEPOSITS) in various tissues. Clinical features include LIVER FAILURE; MULTIPLE MYELOMA; NEPHROTIC SYNDROME; RESTRICTIVE CARDIOMYOPATHY, and neuropathies. subject heading
Number of the records: 1