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Schilderova difúzna cerebrálna skleróza
Record number d002549 Date 06.06.2025 Type M Topical term Schilderova difúzna cerebrálna skleróza Other term English (Pseudonym) Alpers Syndrome
English (Pseudonym) Balo Concentric Sclerosis
English (Pseudonym) Cerebral Sclerosis, Diffuse
English (Pseudonym) Encephalitis Periaxialis
English (Pseudonym) Myelinoclastic Diffuse Sclerosis
English (Pseudonym) Poliodystrophia Cerebri
English (Pseudonym) Schilder Disease
Slovak (Pseudonym) Alpersova difúzna degenerácia šedej mozgovej hmoty s cirhózou pečene
Slovak (Pseudonym) Alpersov syndróm
Slovak (Pseudonym) Alpersova choroba
Slovak (Pseudonym) Alpersova progresívna cerebrálna infantilná poliodystrofia
Slovak (Pseudonym) Alpersova progresívna cerebrálna poliodystrofia detského veku
Slovak (Pseudonym) Alpersov-Huttenlocherov syndróm
Slovak (Pseudonym) Balóova koncentrická skleróza
Slovak (Pseudonym) skleróza mozgová difúzna
Slovak (Pseudonym) skleróza cerebrálna difúzna
Slovak (Pseudonym) encephalitis periaxialis
Slovak (Pseudonym) encefalitída periaxiálna
Slovak (Pseudonym) encephalitis periaxialis concentrica
Slovak (Pseudonym) encefalitída periaxiálna koncentrická
Slovak (Pseudonym) encephalitis periaxialis diffusa
Slovak (Pseudonym) encefalitída periaxiálna difúzna
Slovak (Pseudonym) skleróza myelínoklastická difúzna
Slovak (Pseudonym) poliodystrophia cerebri
Slovak (Pseudonym) poliodystrofia cerebrálna
Slovak (Pseudonym) degenerácia progresívna neuronálna, u detí s ochorením pečene
Slovak (Pseudonym) poliodystrofia progresívna sklerotizujúca
Slovak (Pseudonym) Schilderova choroba
Slovak (Pseudonym) skleróza sudanofilná cerebrálna
UDC C10.114.375.112C10.228.140.400C10.228.140.695.562.112C10.314.350.112C20.111.258.250.175 Note A rare central nervous system demyelinating condition affecting children and young adults. Pathologic findings include a large, sharply defined, asymmetric focus of myelin destruction that may involve an entire lobe or cerebral hemisphere. The clinical course tends to be progressive and includes dementia, cortical blindness, cortical deafness, spastic hemiplegia, and pseudobulbar palsy. Concentric sclerosis of Balo is differentiated from diffuse cerebral sclerosis of Schilder by the pathologic finding of alternating bands of destruction and preservation of myelin in concentric rings. Alpers' Syndrome refers to a heterogeneous group of diseases that feature progressive cerebral deterioration and liver disease. (From Adams et al., Principles of Neurology, 6th ed, p914; Dev Neurosci 1991;13(4-5):267-73) 
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Number of the records: 1