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dysplázia ektodermálna

  1. Record numberd004476
    Date06.06.2025
    TypeM - MESH
    Topical termdysplázia ektodermálna
    Other termEnglish (Pseudonym) Anhidrotic Ectodermal Dysplasia
    English (Pseudonym) Aplasia Cutis Congenita
    English (Pseudonym) Clouston's Syndrome
    English (Pseudonym) Ectodermal Defect, Congenital
    English (Pseudonym) Hidrotic Ectodermal Dysplasia
    Slovak (Pseudonym) dysplázia ektodermová
    Slovak (Pseudonym) dysplázia ektodermová anhidrotická
    Slovak (Pseudonym) dysplázia ektodermálna anhidrotická
    Slovak (Pseudonym) aplasia cutis congenita
    Slovak (Pseudonym) Cloustonov syndróm
    Slovak (Pseudonym) defekt ektodermový kongenitálny
    Slovak (Pseudonym) dysplázia ektodermová hidrotická
    UDCC16.131.077.350C16.131.831.350C16.320.850.250C17.800.804.350C17.800.827.250
    NoteA group of hereditary disorders involving tissues and structures derived from the embryonic ectoderm. They are characterized by the presence of abnormalities at birth and involvement of both the epidermis and skin appendages. They are generally nonprogressive and diffuse. Various forms exist, including anhidrotic and hidrotic dysplasias, FOCAL DERMAL HYPOPLASIA, and aplasia cutis congenita.
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Number of the records: 1  

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