Number of the records: 1
purpura trombotická trombocytopenická
Record number d011697 Date 06.06.2025 Type M - MESH Topical term purpura trombotická trombocytopenická Other term English (Pseudonym) Moschkowitz Disease
English (Pseudonym) Purpura, Thrombotic Thrombopenic
English (Pseudonym) Thrombotic Thrombocytopenic Purpura, Congenital
English (Pseudonym) Thrombotic Thrombocytopenic Purpura, Familial
Slovak (Pseudonym) purpura trombotická trombopenická
Slovak (Pseudonym) purpura trombotická trombocytopenická vrodená
Slovak (Pseudonym) purpura trombotická trombocytopenická kongenitálna
Slovak (Pseudonym) purpura trombotická trombocytopenická familiárna
Slovak (Pseudonym) anémia mikroangiopatická hemolytická vrodená
Slovak (Pseudonym) anémia mikroangiopatická hemolytická kongenitálna
Slovak (Pseudonym) mikroangiopatia trombotická familiárna
Slovak (Pseudonym) Moskowitzova choroba
Slovak (Pseudonym) Moschkowitzova choroba
Slovak (Pseudonym) Schulman-Upshawov syndróm
Slovak (Pseudonym) Upshawov-Schulmanov syndróm
Slovak (Pseudonym) Upshaw-Schulmanov syndróm
Slovak (Pseudonym) deficiencia Upshawovho faktora
Slovak (Pseudonym) deficit Upshawovho faktora
UDC C15.378.100.802.687.680C15.378.140.855.925.750.680C15.378.243.937.925.750.680C15.378.925.850C23.550.414.950.687.680C23.888.885.687.687.680 Note An acquired, congenital, or familial disorder caused by PLATELET AGGREGATION with THROMBOSIS in terminal arterioles and capillaries. Clinical features include THROMBOCYTOPENIA; HEMOLYTIC ANEMIA; AZOTEMIA; FEVER; and thrombotic microangiopathy. The classical form also includes neurological symptoms and end-organ damage, such as RENAL FAILURE. Mutations in the ADAMTS13 PROTEIN gene have been identified in familial cases. subject heading
Number of the records: 1