Number of the records: 1
Wiskottov-Aldrichov syndróm
Record number d014923 Date 06.06.2025 Type M - MESH Topical term Wiskottov-Aldrichov syndróm Other term English (Pseudonym) Aldrich Syndrome
Slovak (Pseudonym) Aldrichov syndróm
UDC C15.378.100.100.970C15.378.243.750.605.900C15.378.463.960C15.378.553.546.605.900C16.320.099.970C16.320.322.937C16.320.798.875C20.673.627.900C20.673.795.875 Note A rare, X-linked immunodeficiency syndrome characterized by ECZEMA; LYMPHOPENIA; and, recurrent pyogenic infection. It is seen exclusively in young boys. Typically, IMMUNOGLOBULIN M levels are low and IMMUNOGLOBULIN A and IMMUNOGLOBULIN E levels are elevated. Lymphoreticular malignancies are common. subject heading
Number of the records: 1