Number of the records: 1
POEMS syndróm
Record number d016878 Date 06.06.2025 Type M - MESH Topical term POEMS syndróm Other term English (Pseudonym) Crow-Fukase Syndrome
English (Pseudonym) Takatsuki's Syndrome
Slovak (Pseudonym) Crowov-Fucaseho syndróm
Slovak (Pseudonym) Takatsukiho syndróm
UDC C10.668.829.800.700C15.378.147.780.750C16.131.077.703C20.683.780.750 Note A multisystemic disorder characterized by a sensorimotor polyneuropathy (POLYNEUROPATHIES), organomegaly, endocrinopathy, monoclonal gammopathy, and pigmentary skin changes. Other clinical features which may be present include EDEMA; CACHEXIA; microangiopathic glomerulopathy; pulmonary hypertension (HYPERTENSION, PULMONARY); cutaneous necrosis; THROMBOCYTOSIS; and POLYCYTHEMIA. This disorder is frequently associated with osteosclerotic myeloma. (From Adams et al., Principles of Neurology, 6th ed, p1335; Rev Med Interne 1997;18(7):553-62) subject heading
Number of the records: 1