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amyloidóza ľahkých reťazcov

  1. Subject h.amyloidóza ľahkých reťazcov
    Subject h.Immunoglobulin Light-chain Amyloidosis
    Entry termschoroba z depozície monoklonových imunoglobulínov
    choroba z ukladania monoklonálnych imunoglobulínov
    AL amyloidóza
    amyloidóza primárna systémová
    amyloidóza z ľahkých reťazcov imunoglobulínu
    amyloidóza primárna
    amyloidóza primárna systémová
    English X referencesMonoclonal Immunoglobulin Deposition Disease
    Scope note in EnglishA nonproliferative disorder of PLASMA CELLS characterized by excessive production and misfolding of IMMUNOGLOBULIN LIGHT CHAINS that form insoluble amyloid fibrils (see AMYLOID DEPOSITS) in various tissues. Clinical features include LIVER FAILURE; MULTIPLE MYELOMA; NEPHROTIC SYNDROME; RESTRICTIVE CARDIOMYOPATHY, and neuropathies.
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