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dentinogenesis imperfecta

  1. Subject h.dentinogenesis imperfecta
    Subject h.Dentinogenesis Imperfecta
    Entry termsdentinogenesis imperfecta hereditaria
    English X referencesHereditary Opalescent Dentin
    Scope note in EnglishAn autosomal dominant disorder of tooth development characterized by opalescent dentin resulting in discoloration of the teeth. The dentin develops poorly with low mineral content while the pulp canal is obliterated.
    See also reference (FX) in Slovak osteogenesis imperfecta
    See also reference (FX) in English Osteogenesis Imperfecta
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    (1) - MeSH descriptor
    (1) - BOOKS
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