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purpura trombotická trombocytopenická

Subject h.	purpura trombotická trombocytopenická
Subject h.	Purpura, Thrombotic Thrombocytopenic
Entry terms	purpura trombotická trombopenická purpura trombotická trombocytopenická vrodená purpura trombotická trombocytopenická kongenitálna purpura trombotická trombocytopenická familiárna anémia mikroangiopatická hemolytická vrodená anémia mikroangiopatická hemolytická kongenitálna mikroangiopatia trombotická familiárna Moskowitzova choroba Moschkowitzova choroba Schulman-Upshawov syndróm Upshawov-Schulmanov syndróm Upshaw-Schulmanov syndróm deficiencia Upshawovho faktora deficit Upshawovho faktora
English X references	Moschkowitz Disease Purpura, Thrombotic Thrombopenic Thrombotic Thrombocytopenic Purpura, Congenital Thrombotic Thrombocytopenic Purpura, Familial
Scope note in English	An acquired, congenital, or familial disorder caused by PLATELET AGGREGATION with THROMBOSIS in terminal arterioles and capillaries. Clinical features include THROMBOCYTOPENIA; HEMOLYTIC ANEMIA; AZOTEMIA; FEVER; and thrombotic microangiopathy. The classical form also includes neurological symptoms and end-organ damage, such as RENAL FAILURE. Mutations in the ADAMTS13 PROTEIN gene have been identified in familial cases.
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