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Criglerov-Najjarov syndróm

  1. Subject h.Criglerov-Najjarov syndróm
    Subject h.Crigler-Najjar Syndrome
    Entry termsCrigler-Najjarov syndróm, typ 1
    Scope note in EnglishA familial form of congenital hyperbilirubinemia transmitted as an autosomal recessive trait. It is characterized by icterus and brain damage caused by a glucuronyl transferase deficiency in the liver and faulty bilirubin conjugation.
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