Number of the records: 1  

purpura trombotická trombocytopenická

  1. SYSd011697
    LBL
      
    00000cx--j2200000---45--
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    20240119195930.6
    100
      
    $a 19990101asloy0103----ba0
    152
      
    $b mesh
    250
      
    $a purpura trombotická trombocytopenická $x BL $x CF $x CI $x CL $x CN $x CO $x DG $x DH $x DI $x DT $x EC $x EH $x EM $x EN $x EP $x ET $x GE $x HI $x IM $x ME $x MI $x MO $x NU $x PA $x PC $x PP $x PS $x PX $x RH $x RT $x SU $x TH $x UR $x VE $x VI $8 slo
    300
    1-
    $a 1986; use PURPURA, THROMBOTIC THROMBOPENIC 1965-1985 $8 eng
    330
    1-
    $a An acquired, congenital, or familial disorder caused by PLATELET AGGREGATION with THROMBOSIS in terminal arterioles and capillaries. Clinical features include THROMBOCYTOPENIA; HEMOLYTIC ANEMIA; AZOTEMIA; FEVER; and thrombotic microangiopathy. The classical form also includes neurological symptoms and end-organ damage, such as RENAL FAILURE. Mutations in the ADAMTS13 PROTEIN gene have been identified in familial cases. $8 eng
    450
      
    $a Moschkowitz Disease $5 e $8 eng
    450
      
    $a Purpura, Thrombotic Thrombopenic $5 e $8 eng
    450
      
    $a Thrombotic Thrombocytopenic Purpura, Congenital $5 e $8 eng
    450
      
    $a Thrombotic Thrombocytopenic Purpura, Familial $5 e $8 eng
    450
      
    $a purpura trombotická trombopenická $5 e $8 slo
    450
      
    $a purpura trombotická trombocytopenická vrodená $5 e $8 slo
    450
      
    $a purpura trombotická trombocytopenická kongenitálna $5 e $8 slo
    450
      
    $a purpura trombotická trombocytopenická familiárna $5 e $8 slo
    450
      
    $a anémia mikroangiopatická hemolytická vrodená $5 e $8 slo
    450
      
    $a anémia mikroangiopatická hemolytická kongenitálna $5 e $8 slo
    450
      
    $a mikroangiopatia trombotická familiárna $5 e $8 slo
    450
      
    $a Moskowitzova choroba $5 e $8 slo
    450
      
    $a Moschkowitzova choroba $5 e $8 slo
    450
      
    $a Schulman-Upshawov syndróm $5 e $8 slo
    450
      
    $a Upshawov-Schulmanov syndróm $5 e $8 slo
    450
      
    $a Upshaw-Schulmanov syndróm $5 e $8 slo
    450
      
    $a deficiencia Upshawovho faktora $5 e $8 slo
    450
      
    $a deficit Upshawovho faktora $5 e $8 slo
    686
      
    $a C15.378.100.802.687.680
    686
      
    $a C15.378.140.855.925.750.680
    686
      
    $a C15.378.243.937.925.750.680
    686
      
    $a C15.378.925.850
    686
      
    $a C23.550.414.950.687.680
    686
      
    $a C23.888.885.687.687.680
    750
      
    $a Purpura, Thrombotic Thrombocytopenic $8 eng
    801
    -0
    $a US $b DNLM $c 19990101
    801
    -2
    $a SK $b BA006 $c 20050727
    801
    -2
    $a SK $b BA006 $c 20110103
    801
    -2
    $a SK $b BA006 $c 20221011
    801
    -2
    $a SK $b BA006 $c 20230925
    980
      
    $x M
Number of the records: 1  

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