Number of the records: 1
purpura trombotická trombocytopenická
SYS d011697 LBL 00000cx--j2200000---45-- 005 20240119195930.6 100 $a 19990101asloy0103----ba0 152 $b mesh 250 $a purpura trombotická trombocytopenická $x BL $x CF $x CI $x CL $x CN $x CO $x DG $x DH $x DI $x DT $x EC $x EH $x EM $x EN $x EP $x ET $x GE $x HI $x IM $x ME $x MI $x MO $x NU $x PA $x PC $x PP $x PS $x PX $x RH $x RT $x SU $x TH $x UR $x VE $x VI $8 slo 300 1-
$a 1986; use PURPURA, THROMBOTIC THROMBOPENIC 1965-1985 $8 eng 330 1-
$a An acquired, congenital, or familial disorder caused by PLATELET AGGREGATION with THROMBOSIS in terminal arterioles and capillaries. Clinical features include THROMBOCYTOPENIA; HEMOLYTIC ANEMIA; AZOTEMIA; FEVER; and thrombotic microangiopathy. The classical form also includes neurological symptoms and end-organ damage, such as RENAL FAILURE. Mutations in the ADAMTS13 PROTEIN gene have been identified in familial cases. $8 eng 450 $a Moschkowitz Disease $5 e $8 eng 450 $a Purpura, Thrombotic Thrombopenic $5 e $8 eng 450 $a Thrombotic Thrombocytopenic Purpura, Congenital $5 e $8 eng 450 $a Thrombotic Thrombocytopenic Purpura, Familial $5 e $8 eng 450 $a purpura trombotická trombopenická $5 e $8 slo 450 $a purpura trombotická trombocytopenická vrodená $5 e $8 slo 450 $a purpura trombotická trombocytopenická kongenitálna $5 e $8 slo 450 $a purpura trombotická trombocytopenická familiárna $5 e $8 slo 450 $a anémia mikroangiopatická hemolytická vrodená $5 e $8 slo 450 $a anémia mikroangiopatická hemolytická kongenitálna $5 e $8 slo 450 $a mikroangiopatia trombotická familiárna $5 e $8 slo 450 $a Moskowitzova choroba $5 e $8 slo 450 $a Moschkowitzova choroba $5 e $8 slo 450 $a Schulman-Upshawov syndróm $5 e $8 slo 450 $a Upshawov-Schulmanov syndróm $5 e $8 slo 450 $a Upshaw-Schulmanov syndróm $5 e $8 slo 450 $a deficiencia Upshawovho faktora $5 e $8 slo 450 $a deficit Upshawovho faktora $5 e $8 slo 686 $a C15.378.100.802.687.680 686 $a C15.378.140.855.925.750.680 686 $a C15.378.243.937.925.750.680 686 $a C15.378.925.850 686 $a C23.550.414.950.687.680 686 $a C23.888.885.687.687.680 750 $a Purpura, Thrombotic Thrombocytopenic $8 eng 801 -0
$a US $b DNLM $c 19990101 801 -2
$a SK $b BA006 $c 20050727 801 -2
$a SK $b BA006 $c 20110103 801 -2
$a SK $b BA006 $c 20221011 801 -2
$a SK $b BA006 $c 20230925 980 $x M
Number of the records: 1