Number of the records: 1
izovaleryl-CoA-dehydrogenáza
SYS d050769 LBL 00000nx--j22000003--45-- 005 20240119200520.7 100 $a 20050630csloy0103----ba0 152 $b mesh 250 $a izovaleryl-CoA-dehydrogenáza $x AD $x AE $x AI $x AN $x BI $x BL $x CF $x CH $x CL $x CS $x DE $x DF $x EC $x GE $x HI $x IM $x IP $x ME $x PD $x PH $x PK $x PO $x RE $x SD $x ST $x TO $x TU $x UL $x UR $8 slo 300 1-
$a 2006(1973) $8 eng 300 1-
$a Acyl Coenzyme A (1980-1982) $8 eng 300 1-
$a Coenzyme A (1973-1980) $8 eng 300 1-
$a Oxidoreductases (1983-2003) $8 eng 300 1-
$a Oxidoreductases Acting on CH-CH Group Donors (2004-2005) $8 eng 300 1-
$a Valerates (1973-1982) $8 eng 330 1-
$a A mitochondrial flavoprotein, this enzyme catalyzes the oxidation of 3-methylbutanoyl-CoA to 3-methylbut-2-enoyl-CoA using FAD as a cofactor. Defects in the enzyme, is associated with isovaleric acidemia (IVA). $8 eng 686 $a D08.811.682.660.462 750 $a Isovaleryl-CoA Dehydrogenase $8 eng 801 -0
$a US $b DNLM $c 20050630 801 -2
$a SK $b BA006 $c 20060731 980 $x M
Number of the records: 1