Isolated Noncompaction of the Ventricular Myocardium
Entry terms
nonkompakcia srdcovej komory, izolovaná non-kompakcia srdcovej komory, izolovaná nekompakcia myokardu ľavej komory, izolovaná nonkompakcia myokardu ľavej komory, izolovaná, viazaná na X-chromozóm nonkompakcia myokardu ľavej komory, izolovaná, autozomálne dominantná nonkompakcia myokardu ľavej komory, izolovaná, autozómovo dominantná
English X references
Isolated Non-compaction of the Ventricular Myocardium Isolated Noncompaction of the Left Ventricular Myocardium, X-Linked Noncompaction of the Left Ventricular Myocardium, Autosomal Dominant
Scope note in English
Rare congenital cardiomyopathies characterized by the lack of left ventricular myocardium compaction. The noncompaction results in numerous prominent trabeculations and a loose myocardial meshwork (spongy myocardium) in the LEFT VENTRICLE. Heterogeneous clinical features include diminished systolic function sometimes associated with left ventricular dilation, that presents either neonatally or progressively. Often, the RIGHT VENTRICLE is also affected. CONGESTIVE HEART FAILURE; PULMONARY EMBOLISM; and ventricular ARRHYTHMIA are commonly seen.
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(4) - ARTICLES
(1) - MeSH descriptor
subject heading
Number of the records: 1
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