Number of the records: 1  

iduronidáza

  1. SYSd007068
    LBL
      
    00000nz--a2200000o--4500
    005
      
    20250606213024.3
    008
      
    921119|||anznnbabn-----------|-a|a------
    040
      
    $b slo $a DNLM $d BA006
    065
      
    $a D08.811.277.450.560
    066
      
    $a 01 $c 03
    150
      
    $a iduronidáza $x AD $x AE $x AI $x AN $x BI $x BL $x CF $x CH $x CL $x CS $x DE $x DF $x EC $x GE $x HI $x IM $x IP $x ME $x PD $x PH $x PK $x PO $x RE $x SD $x ST $x TO $x TU $x UL $x UR $2 slo
    550
      
    $7 sllk_us_auth*d008059 $Y Mucopolysaccharidosis I $w p $a mukopolysacharidóza I
    550
      
    $7 sllk_us_auth*d008059 $Y Mucopolysaccharidosis I $w b $a mukopolysacharidóza I
    665
      
    $a 91(75); was see under GLYCOSIDE HYDROLASES 1975-90 $2 eng
    665
      
    $a Glycoside Hydrolases (1972-1974) $2 eng
    665
      
    $a Hexoses (1972-1974) $2 eng
    665
      
    $a Uronic Acids (1972-1974) $2 eng
    680
    9-
    $i An enzyme that hydrolyzes iduronosidic linkages in desulfated dermatan. Deficiency of this enzyme produces Hurler's syndrome. EC 3.2.1.76. $2 eng
    680
      
    $a /defic: consider also MUCOPOLYSACCHARIDOSIS I $2 eng
    750
    -2
    $a Iduronidase $2 eng
    980
      
    $x M
Number of the records: 1  

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