Number of the records: 1
Creutzfeldtov-Jakobov syndróm
SYS d007562 LBL 00000cz--a2200000n--4500 005 20250606214704.5 008 990101|||anznnbabn-----------|-a|a------ 040 $b slo $a DNLM $d BA006 $d BA006 065 $a C01.207.800.230 065 $a C10.228.140.380.165 065 $a C10.228.228.800.230 065 $a F03.615.400.300 066 $a 01 $c 03 150 $a Creutzfeldtov-Jakobov syndróm $x BL $x CF $x CI $x CL $x CN $x CO $x DG $x DH $x DI $x DT $x EC $x EH $x EM $x EN $x EP $x ET $x GE $x HI $x IM $x ME $x MI $x MO $x NU $x PA $x PC $x PP $x PS $x PX $x RH $x RT $x SU $x TH $x TM $x UR $x VE $x VI $2 slo 450 $w v $a New Variant Creutzfeldt-Jakob Disease $2 eng 450 $w v $a Spongiform Encephalopathy, Subacute $2 eng 450 $w v $a Jakobov-Creutzfeldtov syndróm $2 slo 450 $w v $a vCJD $2 slo 450 $w v $a CJD variantná $2 slo 450 $w v $a Creutzfeldt-Jakobova choroba, nový variant $2 slo 450 $w v $a encefalopatia spongiformná subakútna $2 slo 450 $w v $a encefalopatia spongioformná subakútna $2 slo 450 $w v $a encefalopatia špongiformná subakútna $2 slo 665 $a 1991; use JAKOB-CREUTZFELDT SYNDROME 1981-1990, use CREUTZFELDT-JAKOB DISEASE 1969-1980 $2 eng 665 $a Central Nervous System Diseases (1966-1968) $2 eng 680 9-
$i A rare transmissible encephalopathy most prevalent between the ages of 50 and 70 years. Affected individuals may present with sleep disturbances, personality changes, ATAXIA; APHASIA, visual loss, weakness, muscle atrophy, MYOCLONUS, progressive dementia, and death within one year of disease onset. A familial form exhibiting autosomal dominant inheritance and a new variant CJD (potentially associated with ENCEPHALOPATHY, BOVINE SPONGIFORM) have been described. Pathological features include prominent cerebellar and cerebral cortical spongiform degeneration and the presence of PRIONS. (From N Engl J Med, 1998 Dec 31;339(27)) $2 eng 750 -2
$a Creutzfeldt-Jakob Syndrome $2 eng 980 $x M
Number of the records: 1