Number of the records: 1  

Carneyho komplex

  1. SYSd056733
    LBL
      
    00000nz--a2200000n--4500
    005
      
    20250606220811.7
    008
      
    100101|||anznnbabn-----------|-a|a------
    040
      
    $b slo $a BA006 $a BA006
    065
      
    $a C04.557.450.565.550.312
    065
      
    $a C04.588.894.309.500
    065
      
    $a C14.280.459.500
    065
      
    $a C16.131.077.229
    065
      
    $a C16.131.831.108
    066
      
    $a 01 $c 03
    150
      
    $a Carneyho komplex $x BL $x CF $x CI $x CL $x CO $x DG $x DH $x DI $x DT $x EC $x EH $x EM $x EN $x EP $x ET $x GE $x HI $x IM $x ME $x MI $x MO $x NU $x PA $x PC $x PP $x PS $x PX $x RH $x RT $x SU $x TH $x UR $x VE $x VI $2 slo
    450
      
    $w v $a Carney Complex, Type 2 $2 eng
    450
      
    $w v $a Carney Complex, Type II $2 eng
    450
      
    $w v $a Carney Myxoma-Endocrine Complex $2 eng
    450
      
    $w v $a Carney Syndrome $2 eng
    450
      
    $w v $a LAMB Syndrome $2 eng
    450
      
    $w v $a Myxoma, Spotty Pigmentation, and Endocrine Overactivity $2 eng
    450
      
    $w v $a NAME Syndrome $2 eng
    450
      
    $w v $a Carneyho komplex, typ 2 $2 slo
    450
      
    $w v $a Carneyho komplex typu II $2 slo
    450
      
    $w v $a Carneyho myxóm-endokrinný komplex $2 slo
    450
      
    $w v $a Carneyov syndróm $2 slo
    450
      
    $w v $a LAMB syndróm $2 slo
    450
      
    $w v $a myxóm, pigmentové škvrny a zvýšená endokrinná aktivita $2 slo
    450
      
    $w v $a NAME syndróm $2 slo
    665
      
    $a 2010 $2 eng
    680
    9-
    $i Autosomal dominant syndrome characterized by cardiac and cutaneous MYXOMAS; LENTIGINOSIS (spotty pigmentation of the skin), and endocrinopathy and its associated endocrine tumors. The cardiac myxomas may lead to SUDDEN CARDIAC DEATH and other complications in Carney complex patients. The gene coding for the PRKAR1A protein is one of the causative genetic loci (type 1). A second locus is at chromosome 2p16 (type 2). $2 eng
    750
    -2
    $a Carney Complex $2 eng
    980
      
    $x M
Number of the records: 1  

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