Number of the records: 1
komora ľavá nekompaktná izolovaná
SYS d056830 LBL 00000cz--a2200000n--4500 005 20250606214954.0 008 100101|||anznnbabn-----------|-a|a------ 040 $b slo $a BA006 $a BA006 $d BA006 065 $a C14.240.400.660 065 $a C14.280.238.281.500 065 $a C14.280.400.660 065 $a C16.131.077.477 065 $a C16.131.240.400.655 065 $a C16.320.322.370 066 $a 01 $c 03 150 $a komora ľavá nekompaktná izolovaná $x BL $x CF $x CI $x CL $x CO $x DG $x DH $x DI $x DT $x EC $x EH $x EM $x EN $x EP $x ET $x GE $x HI $x IM $x ME $x MI $x MO $x NU $x PA $x PC $x PP $x PS $x PX $x RH $x RT $x SU $x TH $x UR $x VE $x VI $2 slo 450 $w v $a Isolated Noncompaction of the Left Ventricular Myocardium, X-Linked $2 eng 450 $w v $a Isolated Non-compaction of the Ventricular Myocardium $2 eng 450 $w v $a Noncompaction of the Left Ventricular Myocardium, Autosomal Dominant $2 eng 450 $w v $a nonkompakcia srdcovej komory, izolovaná $2 slo 450 $w v $a non-kompakcia srdcovej komory, izolovaná $2 slo 450 $w v $a nekompakcia myokardu ľavej komory, izolovaná $2 slo 450 $w v $a nonkompakcia myokardu ľavej komory, izolovaná, viazaná na X-chromozóm $2 slo 450 $w v $a nonkompakcia myokardu ľavej komory, izolovaná, autozomálne dominantná $2 slo 450 $w v $a nonkompakcia myokardu ľavej komory, izolovaná, autozómovo dominantná $2 slo 550 $7 sllk_us_auth*d056889 $Y Barth Syndrome $w b $a Barthov syndróm 665 $a 2010 $2 eng 680 9-
$i Rare congenital cardiomyopathies characterized by the lack of left ventricular myocardium compaction. The noncompaction results in numerous prominent trabeculations and a loose myocardial meshwork (spongy myocardium) in the LEFT VENTRICLE. Heterogeneous clinical features include diminished systolic function sometimes associated with left ventricular dilation, that presents either neonatally or progressively. Often, the RIGHT VENTRICLE is also affected. CONGESTIVE HEART FAILURE; PULMONARY EMBOLISM; and ventricular ARRHYTHMIA are commonly seen. $2 eng 750 -2
$a Isolated Noncompaction of the Ventricular Myocardium $2 eng 980 $x M
Number of the records: 1