Number of the records: 1
atrofie olivopontocerebelárne
SYS d009849 LBL 00000cx--j2200000---45-- 005 20240130154524.6 100 $a 19920331asloy0103----ba0 152 $b mesh 250 $a atrofie olivopontocerebelárne $x BL $x CF $x CI $x CL $x CN $x CO $x DG $x DH $x DI $x DT $x EC $x EH $x EM $x EN $x EP $x ET $x GE $x HI $x IM $x ME $x MI $x MO $x NU $x PA $x PC $x PP $x PS $x PX $x RH $x RT $x SU $x TH $x UR $x VE $x VI $8 slo 300 1-
$a 2000(1987) $8 eng 300 1-
$a Atrophy (1966-1986) $8 eng 300 1-
$a Brain Diseases (1966-1986) $8 eng 300 1-
$a Cerebellar Ataxia (1968-1986) $8 eng 300 1-
$a Cerebellar Diseases (1966-1986) $8 eng 300 1-
$a Olivary Nucleus (1966-1986) $8 eng 300 1-
$a Pons (1966-1986) $8 eng 330 1-
$a A group of inherited and sporadic disorders which share progressive ataxia in combination with atrophy of the CEREBELLUM; PONS; and inferior olivary nuclei. Additional clinical features may include MUSCLE RIGIDITY; NYSTAGMUS, PATHOLOGIC; RETINAL DEGENERATION; MUSCLE SPASTICITY; DEMENTIA; URINARY INCONTINENCE; and OPHTHALMOPLEGIA. The familial form has an earlier onset (second decade) and may feature spinal cord atrophy. The sporadic form tends to present in the fifth or sixth decade, and is considered a clinical subtype of MULTIPLE SYSTEM ATROPHY. (From Adams et al., Principles of Neurology, 6th ed, p1085) $8 eng 450 $a Dejerine-Thomas Syndrome $5 e $8 eng 450 $a Olivopontocerebellar Atrophy, Idiopathic $5 e $8 eng 450 $a Olivopontocerebellar Hypoplasia $5 e $8 eng 450 $a atrofia olivopontocereberálna $5 e $8 slo 450 $a Déjerineov-Thomasov syndróm $5 e $8 slo 450 $a Déjerine-Thomasov syndróm $5 e $8 slo 450 $a atrofia olivopontocereberálna familiárna $5 e $8 slo 450 $a atrofia olivopontocereberálna vrodená $5 e $8 slo 450 $a atrofia olivopontocereberálna hereditárna $5 e $8 slo 450 $a atrofia olivopontocerebelárna nefamiliárna $5 e $8 slo 450 $a atrofia olivopontocereberálna idiopatická $5 e $8 slo 450 $a atrofia olivo-ponto-cereberálna $5 e $8 slo 450 $a degenerácia olivo-ponto-cerebelárna $5 e $8 slo 450 $a degenerácia olivopontocerebelárna $5 e $8 slo 450 $a atrofia olivopontocerebelárna $5 e $8 slo 450 $a hypoplázia olivopontocerebelárna $5 e $8 slo 450 $a atrofia pontoolivocerebelárna $5 e $8 slo 450 $a ataxia presenilná $5 e $8 slo 550 $3 sllk_un_auth*d000095747 $Y Olivary Degeneration $5 B $a degenerácia olivárna 550 $3 sllk_un_auth*d000095747 $Y Olivary Degeneration $5 F $a degenerácia olivárna 550 $3 sllk_un_auth*d019578 $Y Multiple System Atrophy $5 B $a atrofia multisystémová 686 $a C10.177.575.550.375 686 $a C10.228.140.079.612.600 686 $a C10.228.140.252.700.650 686 $a C10.228.662.550.600 686 $a C10.228.854.787.750 686 $a C10.574.500.825.650 686 $a C16.320.400.780.750 750 $a Olivopontocerebellar Atrophies $8 eng 801 -0
$a US $b DNLM $c 19920331 801 -2
$a SK $b BA006 $c 20001114 801 -2
$a SK $b BA006 $c 20240130 801 -2
$a SK $b BA006 $c 20240301 980 $x M
Number of the records: 1