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dysplázia ektodermálna
Č. záznamu d004476 Dátum 12.05.2026 Typ M - MESH Tematický termín dysplázia ektodermálna Iný termín Angličtina (Pseudonym) Anhidrotic Ectodermal Dysplasia
Angličtina (Pseudonym) Aplasia Cutis Congenita
Angličtina (Pseudonym) Clouston's Syndrome
Angličtina (Pseudonym) Ectodermal Defect, Congenital
Angličtina (Pseudonym) Hidrotic Ectodermal Dysplasia
Slovenčina (Pseudonym) dysplázia ektodermová
Slovenčina (Pseudonym) dysplázia ektodermová anhidrotická
Slovenčina (Pseudonym) dysplázia ektodermálna anhidrotická
Slovenčina (Pseudonym) aplasia cutis congenita
Slovenčina (Pseudonym) Cloustonov syndróm
Slovenčina (Pseudonym) defekt ektodermový kongenitálny
Slovenčina (Pseudonym) dysplázia ektodermová hidrotická
MDT C16.131.077.350C16.131.831.350C16.320.850.250C17.800.804.350C17.800.827.250 Poznámka A group of hereditary disorders involving tissues and structures derived from the embryonic ectoderm. They are characterized by the presence of abnormalities at birth and involvement of both the epidermis and skin appendages. They are generally nonprogressive and diffuse. Various forms exist, including anhidrotic and hidrotic dysplasias, FOCAL DERMAL HYPOPLASIA, and aplasia cutis congenita. 
predmetové heslo
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