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choroba tenkého čreva, imunoproliferačná
Č. záznamu d007161 Dátum 06.06.2025 Typ M Tematický termín choroba tenkého čreva, imunoproliferačná Iný termín Angličtina (Pseudonym) alpha-Chain Disease
Angličtina (Pseudonym) Heavy Chain Disease, IgA Type
Angličtina (Pseudonym) IPSID
Angličtina (Pseudonym) Lymphoma, Mediterranean
Slovenčina (Pseudonym) choroba z ťažkých reťazcov, IgA typ
Slovenčina (Pseudonym) IPSID
Slovenčina (Pseudonym) lymfóm stredozemný
Slovenčina (Pseudonym) lymphoma mediterraneum
Slovenčina (Pseudonym) choroba ťažkých reťazcov alfa
MDT C04.557.386.390C06.301.371.411.512C06.405.249.411.512C06.405.469.491.505C15.378.147.780.490.512C15.604.515.435.512C20.683.515.512C20.683.780.490.512 Poznámka A condition that is caused by HYPERPLASIA of LYMPHOCYTES in the small intestine (INTESTINE, SMALL) and the mesenteric LYMPH NODES. These lymphocytes produce an anomalous alpha heavy chain protein. Generally, these IPSID patients have either concurrent LYMPHOMA or develop lymphoma within a few years. The disease was first described in the Mediterranean region and is characterized by malabsorption; WEIGHT LOSS; DIARRHEA; and STEATORRHEA. predmetové heslo
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