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purpura trombotická trombocytopenická
Č. záznamu d011697 Dátum 06.06.2025 Typ M - MESH Tematický termín purpura trombotická trombocytopenická Iný termín Angličtina (Pseudonym) Moschkowitz Disease
Angličtina (Pseudonym) Purpura, Thrombotic Thrombopenic
Angličtina (Pseudonym) Thrombotic Thrombocytopenic Purpura, Congenital
Angličtina (Pseudonym) Thrombotic Thrombocytopenic Purpura, Familial
Slovenčina (Pseudonym) purpura trombotická trombopenická
Slovenčina (Pseudonym) purpura trombotická trombocytopenická vrodená
Slovenčina (Pseudonym) purpura trombotická trombocytopenická kongenitálna
Slovenčina (Pseudonym) purpura trombotická trombocytopenická familiárna
Slovenčina (Pseudonym) anémia mikroangiopatická hemolytická vrodená
Slovenčina (Pseudonym) anémia mikroangiopatická hemolytická kongenitálna
Slovenčina (Pseudonym) mikroangiopatia trombotická familiárna
Slovenčina (Pseudonym) Moskowitzova choroba
Slovenčina (Pseudonym) Moschkowitzova choroba
Slovenčina (Pseudonym) Schulman-Upshawov syndróm
Slovenčina (Pseudonym) Upshawov-Schulmanov syndróm
Slovenčina (Pseudonym) Upshaw-Schulmanov syndróm
Slovenčina (Pseudonym) deficiencia Upshawovho faktora
Slovenčina (Pseudonym) deficit Upshawovho faktora
MDT C15.378.100.802.687.680C15.378.140.855.925.750.680C15.378.243.937.925.750.680C15.378.925.850C23.550.414.950.687.680C23.888.885.687.687.680 Poznámka An acquired, congenital, or familial disorder caused by PLATELET AGGREGATION with THROMBOSIS in terminal arterioles and capillaries. Clinical features include THROMBOCYTOPENIA; HEMOLYTIC ANEMIA; AZOTEMIA; FEVER; and thrombotic microangiopathy. The classical form also includes neurological symptoms and end-organ damage, such as RENAL FAILURE. Mutations in the ADAMTS13 PROTEIN gene have been identified in familial cases. predmetové heslo
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