Počet záznamov: 1
retinoblastóm
Č. záznamu d012175 Dátum 06.06.2025 Typ M Tematický termín retinoblastóm Iný termín Angličtina (Pseudonym) Glioblastoma, Retinal
Angličtina (Pseudonym) Glioma, Retinal
Angličtina (Pseudonym) Neuroblastoma, Retinal
Slovenčina (Pseudonym) glioblastóm retiny
Slovenčina (Pseudonym) glióm retiny
Slovenčina (Pseudonym) glioblastóm sietnice
Slovenčina (Pseudonym) glióm sietnice
Pozri tiež (Skutočné meno) gény retinoblastómu
(Novšie záhlavie) gény retinoblastómu
(Novšie záhlavie) nádory sietnice
MDT C04.557.465.625.600.725C04.557.470.670.725C04.557.580.625.600.725C04.588.364.818.760C11.270.862C11.319.475.760C11.768.717.760 Poznámka A malignant tumor arising from the nuclear layer of the retina that is the most common primary tumor of the eye in children. The tumor tends to occur in early childhood or infancy and may be present at birth. The majority are sporadic, but the condition may be transmitted as an autosomal dominant trait. Histologic features include dense cellularity, small round polygonal cells, and areas of calcification and necrosis. An abnormal pupil reflex (leukokoria); NYSTAGMUS, PATHOLOGIC; STRABISMUS; and visual loss represent common clinical characteristics of this condition. (From DeVita et al., Cancer: Principles and Practice of Oncology, 5th ed, p2104) predmetové heslo
Počet záznamov: 1