Počet záznamov: 1
hemoglobinúria paroxyzmálna
SYS d006457 LBL 00000cz--a2200000o--4500 005 20250606214814.3 008 990101|||anznnbabn-----------|-a|a------ 040 $b slo $a DNLM $d BA006 065 $a C15.378.050.141.560 065 $a C15.378.190.625.460 066 $a 01 $c 03 150 $a hemoglobinúria paroxyzmálna $x BL $x CF $x CI $x CL $x CN $x CO $x DG $x DH $x DI $x DT $x EC $x EH $x EM $x EN $x EP $x ET $x GE $x HI $x IM $x ME $x MI $x MO $x NU $x PA $x PC $x PP $x PS $x PX $x RH $x RT $x SU $x TH $x UR $x VE $x VI $2 slo 450 $w v $a Paroxysmal Cold Hemoglobinuria $2 eng 450 $w v $a Paroxysmal Nocturnal Hemoglobinuria $2 eng 450 $w v $a hemoglobinúria paroxyzmálna chladová $2 slo 450 $w v $a hemoglobinúria paroxyzmálna nočná $2 slo 665 $a 78; was MARCHIAFAVA-MICHELI SYNDROME 1963-77 $2 eng 680 9-
$i A condition characterized by the recurrence of HEMOGLOBINURIA caused by intravascular HEMOLYSIS. In cases occurring upon cold exposure (paroxysmal cold hemoglobinuria), usually after infections, there is a circulating antibody which is also a cold hemolysin. In cases occurring during or after sleep (paroxysmal nocturnal hemoglobinuria), the clonal hematopoietic stem cells exhibit a global deficiency of cell membrane proteins. $2 eng 750 -2
$a Hemoglobinuria, Paroxysmal $2 eng 980 $x M
Počet záznamov: 1