Počet záznamov: 1
karbamoylfosfát syntáza (amoniak)
SYS d002222 LBL 00000cx--j2200000---45-- 005 20240119201348.9 100 $a 19921119asloy0103----ba0 152 $b mesh 250 $a karbamoylfosfát syntáza (amoniak) $x AD $x AE $x AI $x AN $x BI $x BL $x CF $x CH $x CL $x CS $x DE $x DF $x EC $x GE $x HI $x IM $x IP $x ME $x PD $x PH $x PK $x PO $x RE $x SD $x ST $x TO $x TU $x UL $x UR $8 slo 300 1-
$a 98(75) $8 eng 300 1-
$a Ammonia (1974) $8 eng 300 1-
$a Carbamates (1974) $8 eng 300 1-
$a Phosphotransferases, ATP (1974) $8 eng 330 1-
$a An enzyme that catalyzes the formation of carbamoyl phosphate from ATP, carbon dioxide, and ammonia. This enzyme is specific for arginine biosynthesis or the urea cycle. Absence or lack of this enzyme may cause CARBAMOYL-PHOSPHATE SYNTHASE I DEFICIENCY DISEASE. EC 6.3.4.16. $8 eng 450 $a Carbamoyl Phosphate Synthetase I $5 e $8 eng 450 $a karbamylfosfátsyntáza (amoniak) $5 e $8 slo 450 $a karbamoylfosfát syntetáza I $5 e $8 slo 450 $a karbamoylfosfátsyntáza (amoniak) $5 e $8 slo 550 $3 sllk_un_auth*d020165 $Y Carbamoyl-Phosphate Synthase I Deficiency Disease $5 F $a choroba z deficitu karbamoylfosfát syntázy I 550 $3 sllk_un_auth*d020165 $Y Carbamoyl-Phosphate Synthase I Deficiency Disease $5 B $a choroba z deficitu karbamoylfosfát syntázy I 686 $a D08.811.464.259.350 750 $a Carbamoyl-Phosphate Synthase (Ammonia) $8 eng 801 -0
$a US $b DNLM $c 19921119 801 -2
$a SK $b BA006 $c 20001117 801 -2
$a SK $b BA006 $c 20200124 820 $a /defic: consider CARBAMOYL-PHOSPHATE SYNTHETASE I DEFICIENCY DISEASE $8 eng 980 $x M
Počet záznamov: 1