Počet záznamov: 1
iduronátsulfatáza
SYS d007066 LBL 00000nx--j22000003--45-- 005 20240119201301.3 100 $a 19920725csloy0103----ba0 152 $b mesh 250 $a iduronátsulfatáza $x AD $x AE $x AI $x AN $x BI $x BL $x CF $x CH $x CL $x CS $x DE $x EC $x GE $x HI $x IM $x IP $x ME $x PD $x PH $x PK $x PO $x RE $x SD $x ST $x TO $x TU $x UL $x UR $8 slo 300 1-
$a 91(76); was see under SULFATASES 1976-90 $8 eng 300 1-
$a Iduronic Acid (1975) $8 eng 300 1-
$a Sulfatases (1972-1975) $8 eng 300 1-
$a Uronic Acids (1972-1975) $8 eng 330 1-
$a An enzyme that specifically cleaves the ester sulfate of iduronic acid. Its deficiency has been demonstrated in Hunter's syndrome, which is characterized by an excess of dermatan sulfate and heparan sulfate. EC 3.1.6.13. $8 eng 450 $a Hunter Corrective Factor $5 e $8 eng 450 $a Iduronatesulfate Sulfohydrolase $5 e $8 eng 450 $a Sulfoiduronate Sulfatase $5 e $8 eng 550 $3 sllk_un_auth*d016532 $Y Mucopolysaccharidosis II $5 F $a mukopolysacharidóza II 550 $3 sllk_un_auth*d016532 $Y Mucopolysaccharidosis II $5 B $a mukopolysacharidóza II 686 $a D08.811.277.352.827.500 750 $a Iduronate Sulfatase $8 eng 801 -0
$a US $b DNLM $c 19920725 801 -2
$a SK $b BA006 $c 20070706 980 $x M
Počet záznamov: 1