Počet záznamov: 1
uroporfyrinogéndekarboxyláza
SYS d014575 LBL 00000nx--j22000003--45-- 005 20240119200048.8 100 $a 19920725csloy0103----ba0 152 $b mesh 250 $a uroporfyrinogéndekarboxyláza $x AD $x AE $x AI $x AN $x BI $x BL $x CF $x CH $x CL $x CS $x DE $x DF $x EC $x GE $x HI $x IM $x IP $x ME $x PD $x PH $x PK $x PO $x RE $x SD $x ST $x TO $x TU $x UL $x UR $8 slo 300 1-
$a 91(76); was see under CARBOXY-LYASES 1976-90 $8 eng 300 1-
$a Carboxy-Lyases (1974-1975) $8 eng 300 1-
$a Porphyrinogens (1975) $8 eng 300 1-
$a Porphyrins (1974) $8 eng 330 1-
$a An enzyme that catalyzes the decarboxylation of UROPORPHYRINOGEN III to coproporphyrinogen III by the conversion of four acetate groups to four methyl groups. It is the fifth enzyme in the 8-enzyme biosynthetic pathway of HEME. Several forms of cutaneous PORPHYRIAS are results of this enzyme deficiency as in PORPHYRIA CUTANEA TARDA; and HEPATOERYTHROPOIETIC PORPHYRIA. $8 eng 450 $a Uroporphyrinogen Carboxy-Lyase $5 e $8 eng 450 $a uroporfyrinogénkarboxylyáza $5 e $8 slo 686 $a D08.811.520.224.125.900 750 $a Uroporphyrinogen Decarboxylase $8 eng 801 -0
$a US $b DNLM $c 19920725 801 -2
$a SK $b BA006 $c 20070706 820 $a /defic permitted but consider also PORPHYRIA CUTANEA TARDA and HEPATOERYTHROPOIETIC PORPHYRIA $8 eng 980 $x M
Počet záznamov: 1