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Wiskottov-Aldrichov syndróm
SYS d014923 LBL 00000nx--j22000003--45-- 005 20240119200058.3 100 $a 19990101csloy0103----ba0 152 $b mesh 250 $a Wiskottov-Aldrichov syndróm $x BL $x CF $x CI $x CL $x CO $x DG $x DH $x DI $x DT $x EC $x EH $x EM $x EN $x EP $x ET $x GE $x HI $x IM $x ME $x MI $x MO $x NU $x PA $x PC $x PP $x PS $x PX $x RH $x RT $x SU $x TH $x UR $x VE $x VI $8 slo 300 1-
$a 85; was ALDRICH SYNDROME 1963-84 $8 eng 330 1-
$a A rare, X-linked immunodeficiency syndrome characterized by ECZEMA; LYMPHOPENIA; and, recurrent pyogenic infection. It is seen exclusively in young boys. Typically, IMMUNOGLOBULIN M levels are low and IMMUNOGLOBULIN A and IMMUNOGLOBULIN E levels are elevated. Lymphoreticular malignancies are common. $8 eng 450 $a Aldrich Syndrome $5 e $8 eng 450 $a Aldrichov syndróm $5 e $8 slo 686 $a C15.378.100.100.970 686 $a C15.378.243.750.605.900 686 $a C15.378.463.960 686 $a C15.378.553.546.605.900 686 $a C16.320.099.970 686 $a C16.320.322.937 686 $a C16.320.798.875 686 $a C20.673.627.900 686 $a C20.673.795.875 750 $a Wiskott-Aldrich Syndrome $8 eng 801 -0
$a US $b DNLM $c 19990101 801 -2
$a SK $b BA006 $c 20070706 980 $x M
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