Počet záznamov: 1
kraniofaryngeóm
Č. záznamu d003397 Dátum 06.06.2025 Typ M Tematický termín kraniofaryngeóm Iný termín Angličtina (Pseudonym) Craniopharyngioma, Adamantinous
Angličtina (Pseudonym) Craniopharyngioma, Papillary
Angličtina (Pseudonym) Rathke Pouch Tumor
Slovenčina (Pseudonym) kraniofaryngeóm adamantinózny
Slovenčina (Pseudonym) kraniofaryngeóm papilárny
Slovenčina (Pseudonym) nádor Rathkeho puzdra
MDT C04.557.465.625.200C04.557.580.625.200 Poznámka A benign pituitary-region neoplasm that originates from Rathke's pouch. The two major histologic and clinical subtypes are adamantinous (or classical) craniopharyngioma and papillary craniopharyngioma. The adamantinous form presents in children and adolescents as an expanding cystic lesion in the pituitary region. The cystic cavity is filled with a black viscous substance and histologically the tumor is composed of adamantinomatous epithelium and areas of calcification and necrosis. Papillary craniopharyngiomas occur in adults, and histologically feature a squamous epithelium with papillations. (From Joynt, Clinical Neurology, 1998, Ch14, p50) predmetové heslo
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