Počet záznamov: 1
purpura trombotická trombocytopenická
SYS d011697 LBL 00000cz--a2200000n--4500 005 20250606214444.4 008 990101|||anznnbabn-----------|-a|a------ 040 $b slo $a DNLM $d BA006 $d BA006 $d BA006 $d BA006 065 $a C15.378.100.802.687.680 065 $a C15.378.140.855.925.750.680 065 $a C15.378.243.937.925.750.680 065 $a C15.378.925.850 065 $a C23.550.414.950.687.680 065 $a C23.888.885.687.687.680 066 $a 01 $c 03 150 $a purpura trombotická trombocytopenická $x BL $x CF $x CI $x CL $x CN $x CO $x DG $x DH $x DI $x DT $x EC $x EH $x EM $x EN $x EP $x ET $x GE $x HI $x IM $x ME $x MI $x MO $x NU $x PA $x PC $x PP $x PS $x PX $x RH $x RT $x SU $x TH $x UR $x VE $x VI $2 slo 450 $w v $a Moschkowitz Disease $2 eng 450 $w v $a Purpura, Thrombotic Thrombopenic $2 eng 450 $w v $a Thrombotic Thrombocytopenic Purpura, Congenital $2 eng 450 $w v $a Thrombotic Thrombocytopenic Purpura, Familial $2 eng 450 $w v $a purpura trombotická trombopenická $2 slo 450 $w v $a purpura trombotická trombocytopenická vrodená $2 slo 450 $w v $a purpura trombotická trombocytopenická kongenitálna $2 slo 450 $w v $a purpura trombotická trombocytopenická familiárna $2 slo 450 $w v $a anémia mikroangiopatická hemolytická vrodená $2 slo 450 $w v $a anémia mikroangiopatická hemolytická kongenitálna $2 slo 450 $w v $a mikroangiopatia trombotická familiárna $2 slo 450 $w v $a Moskowitzova choroba $2 slo 450 $w v $a Moschkowitzova choroba $2 slo 450 $w v $a Schulman-Upshawov syndróm $2 slo 450 $w v $a Upshawov-Schulmanov syndróm $2 slo 450 $w v $a Upshaw-Schulmanov syndróm $2 slo 450 $w v $a deficiencia Upshawovho faktora $2 slo 450 $w v $a deficit Upshawovho faktora $2 slo 665 $a 1986; use PURPURA, THROMBOTIC THROMBOPENIC 1965-1985 $2 eng 680 9-
$i An acquired, congenital, or familial disorder caused by PLATELET AGGREGATION with THROMBOSIS in terminal arterioles and capillaries. Clinical features include THROMBOCYTOPENIA; HEMOLYTIC ANEMIA; AZOTEMIA; FEVER; and thrombotic microangiopathy. The classical form also includes neurological symptoms and end-organ damage, such as RENAL FAILURE. Mutations in the ADAMTS13 PROTEIN gene have been identified in familial cases. $2 eng 750 -2
$a Purpura, Thrombotic Thrombocytopenic $2 eng 980 $x M
Počet záznamov: 1