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POEMS syndróm
Č. záznamu d016878 Dátum 06.06.2025 Typ M - MESH Tematický termín POEMS syndróm Iný termín Angličtina (Pseudonym) Crow-Fukase Syndrome
Angličtina (Pseudonym) Takatsuki's Syndrome
Slovenčina (Pseudonym) Crowov-Fucaseho syndróm
Slovenčina (Pseudonym) Takatsukiho syndróm
MDT C10.668.829.800.700C15.378.147.780.750C16.131.077.703C20.683.780.750 Poznámka A multisystemic disorder characterized by a sensorimotor polyneuropathy (POLYNEUROPATHIES), organomegaly, endocrinopathy, monoclonal gammopathy, and pigmentary skin changes. Other clinical features which may be present include EDEMA; CACHEXIA; microangiopathic glomerulopathy; pulmonary hypertension (HYPERTENSION, PULMONARY); cutaneous necrosis; THROMBOCYTOSIS; and POLYCYTHEMIA. This disorder is frequently associated with osteosclerotic myeloma. (From Adams et al., Principles of Neurology, 6th ed, p1335; Rev Med Interne 1997;18(7):553-62) predmetové heslo
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