Počet záznamov: 1  

neoplázia endokrinná mnohopočetná, typ 2b

  1. SYSd018814
    LBL
      
    00000cz--a2200000o--4500
    005
      
    20250606214148.1
    008
      
    940523|||anznnbabn-----------|-a|a------
    040
      
    $b slo $a DNLM $d BA006
    065
      
    $a C04.588.322.400.510
    065
      
    $a C04.651.600.510
    065
      
    $a C04.700.630.510
    065
      
    $a C16.320.700.630.510
    065
      
    $a C19.344.400.510
    066
      
    $a 01 $c 03
    150
      
    $a neoplázia endokrinná mnohopočetná, typ 2b $x BL $x BS $x CF $x CH $x CI $x CL $x CN $x CO $x DG $x DH $x DI $x DT $x EC $x EH $x EM $x EN $x EP $x ET $x GE $x HI $x IM $x ME $x MI $x MO $x NU $x PA $x PC $x PP $x PS $x PX $x RH $x RT $x SC $x SU $x TH $x UL $x UR $x VE $x VI $2 slo
    450
      
    $w v $a MEN 2b $2 eng
    450
      
    $w v $a MEN 3 $2 eng
    450
      
    $w v $a Neoplasia, Multiple Endocrine Type 2b $2 eng
    450
      
    $w v $a Neoplasms, Multiple Endocrine Type 2b $2 eng
    450
      
    $w v $a nádory endokrinné mnohopočetné, typ 2b $2 slo
    450
      
    $w v $a MEN2b $2 slo
    450
      
    $w v $a MEN 2b $2 slo
    450
      
    $w v $a MEN 3 $2 slo
    550
      
    $7 sllk_us_auth*d010673 $Y Pheochromocytoma $w b $a feochromocytóm
    550
      
    $7 sllk_us_auth*d018276 $Y Carcinoma, Medullary $w b $a karcinóm medulárny
    665
      
    $a 1995; MEA III & MEN III see NEOPLASMS, MULTIPLE ENDOCRINE 1983-1994 $2 eng
    665
      
    $a Multiple Endocrine Neoplasia (1975-1994) $2 eng
    680
    9-
    $i Similar to MEN2A, it is also caused by mutations of the MEN2 gene, also known as the RET proto-oncogene. Its clinical symptoms include medullary carcinoma (CARCINOMA, MEDULLARY) of THYROID GLAND and PHEOCHROMOCYTOMA of ADRENAL MEDULLA (50%). Unlike MEN2a, MEN2b does not involve PARATHYROID NEOPLASMS. It can be distinguished from MEN2A by its neural abnormalities such as mucosal NEUROMAS on EYELIDS; LIP; and TONGUE, and ganglioneuromatosis of GASTROINTESTINAL TRACT leading to MEGACOLON. It is an autosomal dominant inherited disease. $2 eng
    680
      
    $a coordinate IM with specific endocrine/neoplasm pre-coordinates (IM) + specific histological type (IM) if pertinent $2 eng
    750
    -2
    $a Multiple Endocrine Neoplasia Type 2b $2 eng
    980
      
    $x M
Počet záznamov: 1  

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