Počet záznamov: 1  

glutaryl-CoA-dehydrogenáza

  1. SYSd050770
    LBL
      
    00000nz--a2200000o--4500
    005
      
    20250606214851.5
    008
      
    050630|||anznnbabn-----------|-a|a------
    040
      
    $b slo $a DNLM $d BA006
    065
      
    $a D08.811.682.660.425
    066
      
    $a 01 $c 03
    150
      
    $a glutaryl-CoA-dehydrogenáza $x AD $x AE $x AI $x AN $x BI $x BL $x CF $x CH $x CL $x CS $x DE $x DF $x EC $x GE $x HI $x IM $x IP $x ME $x PD $x PH $x PK $x PO $x RE $x SD $x ST $x TO $x TU $x UL $x UR $2 slo
    665
      
    $a 2006(1973) $2 eng
    665
      
    $a Acyl Coenzyme A (1973-1979) $2 eng
    665
      
    $a Coenzymes (1973-1979) $2 eng
    665
      
    $a Glutarates (1973-1980) $2 eng
    665
      
    $a Oxidoreductases (1983-2003) $2 eng
    665
      
    $a Oxidoreductases Acting on CH-CH Group Donors (2004-2005) $2 eng
    680
    9-
    $i A flavoprotein enzyme that is responsible for the catabolism of LYSINE; HYDROXYLYSINE; and TRYPTOPHAN. It catalyzes the oxidation of GLUTARYL-CoA to crotonoyl-CoA using FAD as a cofactor. Glutaric aciduria type I is an inborn error of metabolism due to the deficiency of glutaryl-CoA dehydrogenase. $2 eng
    750
    -2
    $a Glutaryl-CoA Dehydrogenase $2 eng
    980
      
    $x M
Počet záznamov: 1  

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