Počet záznamov: 1
koproporfyrinogénoxidáza
SYS d003304 LBL 00000nx--j22000003--45-- 005 20240119195549.2 100 $a 19920725csloy0103----ba0 152 $b mesh 250 $a koproporfyrinogénoxidáza $x AD $x AE $x AI $x AN $x BI $x BL $x CF $x CH $x CL $x CS $x DE $x EC $x GE $x HI $x IM $x IP $x ME $x PD $x PH $x PK $x PO $x RE $x SD $x ST $x TO $x TU $x UL $x UR $8 slo 300 1-
$a 91(76); was see under OXIDOREDUCTASES 1976-90 $8 eng 300 1-
$a Carboxy-Lyases (1972-1974) $8 eng 300 1-
$a Coproporphyrins (1975) $8 eng 300 1-
$a Oxidoreductases (1975) $8 eng 300 1-
$a Porphyrins (1972-1974) $8 eng 330 1-
$a An enzyme that catalyzes the oxidative decarboxylation of coproporphyrinogen III to protoporphyrinogen IX by the conversion of two propionate groups to two vinyl groups. It is the sixth enzyme in the 8-enzyme biosynthetic pathway of HEME, and is encoded by CPO gene. Mutations of CPO gene result in HEREDITARY COPROPORPHYRIA. $8 eng 450 $a Coproporphyrinogenase $5 e $8 eng 686 $a D08.811.682.660.250 750 $a Coproporphyrinogen Oxidase $8 eng 801 -0
$a US $b DNLM $c 19920725 801 -2
$a SK $b BA006 $c 20070706 980 $x M
Počet záznamov: 1