Počet záznamov: 1
hemoglobinúria paroxyzmálna
SYS d006457 LBL 00000cx--j22000003--45-- 005 20240119195712.9 100 $a 19990101csloy0103----ba0 152 $b mesh 250 $a hemoglobinúria paroxyzmálna $x BL $x CF $x CI $x CL $x CN $x CO $x DG $x DH $x DI $x DT $x EC $x EH $x EM $x EN $x EP $x ET $x GE $x HI $x IM $x ME $x MI $x MO $x NU $x PA $x PC $x PP $x PS $x PX $x RH $x RT $x SU $x TH $x UR $x VE $x VI $8 slo 300 1-
$a 78; was MARCHIAFAVA-MICHELI SYNDROME 1963-77 $8 eng 330 1-
$a A condition characterized by the recurrence of HEMOGLOBINURIA caused by intravascular HEMOLYSIS. In cases occurring upon cold exposure (paroxysmal cold hemoglobinuria), usually after infections, there is a circulating antibody which is also a cold hemolysin. In cases occurring during or after sleep (paroxysmal nocturnal hemoglobinuria), the clonal hematopoietic stem cells exhibit a global deficiency of cell membrane proteins. $8 eng 450 $a Paroxysmal Cold Hemoglobinuria $5 e $8 eng 450 $a Paroxysmal Nocturnal Hemoglobinuria $5 e $8 eng 450 $a hemoglobinúria paroxyzmálna chladová $5 e $8 slo 450 $a hemoglobinúria paroxyzmálna nočná $5 e $8 slo 686 $a C15.378.050.141.560 686 $a C15.378.190.625.460 750 $a Hemoglobinuria, Paroxysmal $8 eng 801 -0
$a US $b DNLM $c 19990101 801 -2
$a SK $b BA006 $c 20070227 980 $x M
Počet záznamov: 1