Počet záznamov: 1  

hemoglobinúria paroxyzmálna

  1. SYSd006457
    LBL
      
    00000cx--j22000003--45--
    005
      
    20240119195712.9
    100
      
    $a 19990101csloy0103----ba0
    152
      
    $b mesh
    250
      
    $a hemoglobinúria paroxyzmálna $x BL $x CF $x CI $x CL $x CN $x CO $x DG $x DH $x DI $x DT $x EC $x EH $x EM $x EN $x EP $x ET $x GE $x HI $x IM $x ME $x MI $x MO $x NU $x PA $x PC $x PP $x PS $x PX $x RH $x RT $x SU $x TH $x UR $x VE $x VI $8 slo
    300
    1-
    $a 78; was MARCHIAFAVA-MICHELI SYNDROME 1963-77 $8 eng
    330
    1-
    $a A condition characterized by the recurrence of HEMOGLOBINURIA caused by intravascular HEMOLYSIS. In cases occurring upon cold exposure (paroxysmal cold hemoglobinuria), usually after infections, there is a circulating antibody which is also a cold hemolysin. In cases occurring during or after sleep (paroxysmal nocturnal hemoglobinuria), the clonal hematopoietic stem cells exhibit a global deficiency of cell membrane proteins. $8 eng
    450
      
    $a Paroxysmal Cold Hemoglobinuria $5 e $8 eng
    450
      
    $a Paroxysmal Nocturnal Hemoglobinuria $5 e $8 eng
    450
      
    $a hemoglobinúria paroxyzmálna chladová $5 e $8 slo
    450
      
    $a hemoglobinúria paroxyzmálna nočná $5 e $8 slo
    686
      
    $a C15.378.050.141.560
    686
      
    $a C15.378.190.625.460
    750
      
    $a Hemoglobinuria, Paroxysmal $8 eng
    801
    -0
    $a US $b DNLM $c 19990101
    801
    -2
    $a SK $b BA006 $c 20070227
    980
      
    $x M
Počet záznamov: 1  

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