Počet záznamov: 1
komora ľavá nekompaktná izolovaná
SYS d056830 LBL 00000cx--j2200000---45-- 005 20240119201506.5 100 $a 20100101asloy0103----ba0 152 $b mesh 250 $a komora ľavá nekompaktná izolovaná $x BL $x CF $x CI $x CL $x CO $x DG $x DH $x DI $x DT $x EC $x EH $x EM $x EN $x EP $x ET $x GE $x HI $x IM $x ME $x MI $x MO $x NU $x PA $x PC $x PP $x PS $x PX $x RH $x RT $x SU $x TH $x UR $x VE $x VI $8 slo 300 1-
$a 2010 $8 eng 330 1-
$a Rare congenital cardiomyopathies characterized by the lack of left ventricular myocardium compaction. The noncompaction results in numerous prominent trabeculations and a loose myocardial meshwork (spongy myocardium) in the LEFT VENTRICLE. Heterogeneous clinical features include diminished systolic function sometimes associated with left ventricular dilation, that presents either neonatally or progressively. Often, the RIGHT VENTRICLE is also affected. CONGESTIVE HEART FAILURE; PULMONARY EMBOLISM; and ventricular ARRHYTHMIA are commonly seen. $8 eng 450 $a Isolated Non-compaction of the Ventricular Myocardium $5 e $8 eng 450 $a Isolated Noncompaction of the Left Ventricular Myocardium, X-Linked $5 e $8 eng 450 $a Noncompaction of the Left Ventricular Myocardium, Autosomal Dominant $5 e $8 eng 450 $a nonkompakcia srdcovej komory, izolovaná $5 e $8 slo 450 $a non-kompakcia srdcovej komory, izolovaná $5 e $8 slo 450 $a nekompakcia myokardu ľavej komory, izolovaná $5 e $8 slo 450 $a nonkompakcia myokardu ľavej komory, izolovaná, viazaná na X-chromozóm $5 e $8 slo 450 $a nonkompakcia myokardu ľavej komory, izolovaná, autozomálne dominantná $5 e $8 slo 450 $a nonkompakcia myokardu ľavej komory, izolovaná, autozómovo dominantná $5 e $8 slo 550 $3 sllk_un_auth*d056889 $Y Barth Syndrome $5 B $a Barthov syndróm 686 $a C14.240.400.660 686 $a C14.280.238.281.500 686 $a C14.280.400.660 686 $a C16.131.077.477 686 $a C16.131.240.400.655 686 $a C16.320.322.370 750 $a Isolated Noncompaction of the Ventricular Myocardium $8 eng 801 -0
$a SK $b BA006 $c 20100316 801 -0
$a SK $b BA006 $c 20100805 801 -2
$a SK $b BA006 $c 20130603 980 $x M
Počet záznamov: 1