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neurofibrosarkóm
Subject h. neurofibrosarkóm Subject h. Neurofibrosarcoma Entry terms MPNST
neurilemóm malígny
sarkóm neurogénny
neurilemmosarkóm
nádory z nervových obalov periférnych nervov, malígne
nádory z myelínovej pošvy periférnych nervov, malígne
schwannóm malígnyEnglish X references Malignant Peripheral Nerve Sheath Tumors
Neurilemmosarcoma
Sarcoma, NeurogenicScope note in English A malignant tumor that arises from small cutaneous nerves, is locally aggressive, and has a potential for metastasis. Characteristic histopathologic features include proliferating atypical spindle cells with slender wavy and pointed nuclei, hypocellular areas, and areas featuring organized whorls of fibroblastic proliferation. The most common primary sites are the extremities, retroperitoneum, and trunk. These tumors tend to present in childhood, often in association with NEUROFIBROMATOSIS 1. (From DeVita et al., Cancer: Principles & Practice of Oncology, 5th ed, p1662; Mayo Clin Proc 1990 Feb;65(2):164-72) subject heading
Number of the records: 1